Abstract
Author(s): Reza Ahadi, Nader Tavakoli, Pegah Babaheidarian, Yusef Abbasi
The Primitive neuroectodermal tumor (PNET) is a malignant tumor which arises from neural crest cells. It is a rare tumor, usually occurring in children and young adults. PNET Categorized in the same tumor family as Ewing sarcoma which occur in bones and soft tissues. A small number of PNET cases arising in the pelvic organs like as uterine corpus, ovaries, cervix, and vulva in the broad ligament have been reported. We present a case of pelvic PNET in the left ovary with adhesion to the surrounding organs associated with para aortic lymphadenopathy. The site and volume of tumor, and presence or absence of metastasis are prognostic factors of PNET. PNET is a malignant tumor which has lymphatic and haematogenous metastases. Although the local tumor irradiation could be a radical treatment even in some cases but some of them requires surgical resection and chemotherapy.